Lipidosis


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Lipidosis,
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a group of disorders characterized by abnormal accumulation of lipids within reticuloendothelial cells (Table 1).

Lipiodosis, Table 1. Lipid storage disease

Gauchers disease (glycosylceramide lipiodosis)
Niemann Pick disease (sphingomyelin lipidosis)
Fabrys disease (glycolipidosis)
Refsums disease (phytanic acid storage disease)
Krabbes disease (galactosylceramide lipidosis)
Metachromatic leukodystrophy (sulphatide lipidosis)
Farber's lipogranulomatosis (ceramidase deficiency)
Gangliosidosis
Sea-blue histiocytosis
Tay Sachs disease
Fucosidosis

The disorders are discussed more fully under their specific names.


DR


The Encyclopaedia of Medical Imaging Volume III 1